Polysplenia Syndrome Associated with Situs Inversus Abdominus and Type I Jejunal Atresia

نویسندگان

  • Farooq Rasool
  • Bilal Mirza
چکیده

Polysplenia is a presence of two or more spleens in a patient and polysplenia syndrome refers to its association with various organ abnormalities in abdomen and chest. In about 20% cases of polysplenia syndrome situs inversus is present [1]. Polysplenia syndrome in association with situs inversus abdominus and intestinal atresia is rarely reported. We are presenting a case of polysplenia syndrome associated with situs inversus abdominus and type-I jejunal atresia.

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

Biliary Atresia Associated with Polysplenia Syndrome, Situs Inversus Abdominus, and Reverse Rotation of Intestine

In 25% of cases of biliary atresia associated malformations are present; polysplenia constitute 10-50% of these associated anomalies. Biliary atresia found associated with polysplenia syndrome, heterotaxy, and reverse rotation of intestine, in isolation or in various combinations; however its association with polysplenia syndrome, situs inversus abdominus, and reverse rotation of gut in the sam...

متن کامل

Duodenal Atresia Associated with Apple Peel Atresia and Situs Inversus Abdominus: A Case Report

Duodenal atresia is rarely associated with situs inversus abdominus. We report a case of duodenal atresia associated with small bowel atresia of apple peel type and situs inversus abdominus.

متن کامل

Biliary Atresia Associated with Polysplenia Syndrome, Dextrocardia, Situs Inversus Totalis and Malrotation of Intestines

Biliary atresia (BA) is a rare disease and the end result of a destructive, inflammatory cholangiopathy, leading to fibrosis and biliary cirrhosis. It is classified into syndromic variety with various congenital anomalies and non-syndromic (isolated anomaly). We present here a 1-month-old female child with the syndromic variety of BA associated with polysplenia syndrome, dextrocardia, situs inv...

متن کامل

Asplenia and polysplenia syndromes with abnormalities of lateralisation in a sibship.

In the family presented here the first child had asplenia syndrome with cor biloculare' transposition of the great vessels, pulmonary stenosis, and anomalous pulmonary venous drainage. Another sib had situs inversus with polysplenia syndrome, including very similar cardiovascular defects and biliary atresia. The possibility that these two syndromes, namely asplenia and polysplenia, are differen...

متن کامل

Polysplenia Syndrome Associated With Heterotaxy of Abdominal Viscera and Type IV Intestinal Atresias

Polysplenia syndrome in association with situs inversus and intestinal atresia is rarely reported [1]. A 2-day-old male neonate was presented with neonatal intestinal obstruction. Abdominal radiograph showed air fluid levels suggestive of small bowel atresia. Ultrasound of the abdomen showed dilated bowel loops throughout the abdominal cavity. At operation, there was right sided stomach, centra...

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

عنوان ژورنال:

دوره 2  شماره 

صفحات  -

تاریخ انتشار 2011